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Description
2500 * L-Carnitine , ,

Friedman, S

Jackson J
Teppola, H., Selinummi, J., Sarkanen,J.R., Pettinen, A., Jalonen, T.O., Yli-Harja, O., Linne, M.L

In PA, loss-of-function mutations in PCCA or PCCB result in reduced or absent propionyl-CoA carboxylase (PCC) activity 7 , which hinders propionyl-CoA catabolism
